Idiopathic pulmonary hemosiderosis: presentation of an atypical case

Idiopathic pulmonary hemosiderosis: presentation of an atypical case

José P. Unda-Haro 1, Ma. Isabel Peinado-Fabregat 2, Juan R. Osegueda-Mayen 3

1 Pediatría, Grupo Médico Pediátrico, Ciudad de México, México; 2 General Pediatrics, Stanford School of Medicine, Palo Alto, California, United States; Academic Pediatric Association; Ciudad de México, México; 3 Pediatría y Neonatología, Grupo Médico Pediátrico. Ciudad de México, México

*Correspondence: José P. Unda-Haro. Email: jpunda89@gmail.com

Abstract

Idiopathic pulmonary hemosiderosis is a rare disease that usually presents in children and is characterized by recurrent pulmonary hemorrhages which cause the triad of hemoptysis, anemia, and pulmonary infiltrates on imaging studies. We present a clinical case of a 17-month-old male who presented with cough, respiratory distress, and requiring supplemental oxygen to maintain adequate oxygen saturation. Imaging studies were significant for a diffuse interstitial pattern, which prompted a bronchoscopy, where hemosiderin laden macrophages were found. First line of treatment was started with immunomodulators as well as anti-inflammatories such as topical and systemic steroids. Due to the poor therapeutic response, a pulmonary biopsy was pursued which demonstrated episodes of recent bleeding and specific histopathological changes confirming the diagnosis of early idiopathic pulmonary hemosiderosis.

Keywords: Cough. Hemosiderosis. Pneumonia.

Contents

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